Pulmonary Alveolar Proteinosis
National Organization for Rare Disorders, Inc.
- Alveolar Lipoproteinosis
- Idiopathic Pulmonary Alveolar Proteinosis
- Secondary Pulmonary Alveolar Proteinosis
- Congenital Pulmonary Alveolar Proteinosis
Pulmonary alveolar proteinosis (PAP) is a rare lung disorder characterized by the accumulation of grainy material consisting mostly of protein and fat (lipoproteinaceous material) in the air sacs of the lungs (alveoli). Breathing often becomes progressively difficult. The disorder occurs in different forms, ranging from mild to severe, and can affect individuals of any age. PAP may occur secondary to many environmental exposures or underlying diseases. However, most cases of PAP occur for no known reason (idiopathic or primary PAP). An extremely rare form of PAP occurs in newborns (congenital PAP).
American Lung Association
1301 Pennsylvania Ave NW
Washington, DC 20004
NIH/National Heart, Lung and Blood Institute
P.O. Box 30105
Bethesda, MD 20892-0105
Genetic and Rare Diseases (GARD) Information Center
PO Box 8126
Gaithersburg, MD 20898-8126
British Paediatric Orphan Lung Disease
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Last Updated: 5/6/2008
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