How should I take ivacaftor?
Follow all directions on your prescription label and read all medication guides or instruction sheets. Use the medicine exactly as directed.
Take ivacaftor with food that contains fat, such as butter, peanut butter, eggs, cheese, whole milk, yogurt, or cheese pizza. Follow your doctor's instructions very carefully.
To use ivacaftor oral granules: Mix the granules with 1 teaspoon of liquid or soft food such as water, juice, milk, pudding, yogurt, or applesauce. Mix only 1 dose at a time, and use the mixture within 1 hour after mixing. Feed the child a high-fat food just before or just after giving the granule mixture.
Take your doses at regular intervals, 12 hours apart.
Ivacaftor doses are based on age and weight in children. Children from 4 months to 5 years old should take oral granules. Children 6 and older should take tablets.
You will need frequent blood tests to check your liver function.
A child using this medicine may need frequent eye exams.
Store at room temperature away from moisture and heat. Keep each tablet in the foil blister pack until you are ready to take it.